Recurrent Painful Ophthalmoplegic Neuropathy Affecting Right Oculomotor Nerve in 10-Year-Old Male. Case Report

Authors

  • Sharmila Segar Medical College of Georgia, Augusta University, Augusta, Georgia, USA.
  • Chandni Duphare Medical College of Georgia, Augusta University, Augusta, Georgia, USA.
  • Osemelu Aburime Medical College of Georgia, Augusta University, Augusta, Georgia, USA.

DOI:

https://doi.org/10.5195/ijms.2018.285

Keywords:

Ophthalmoplegic Migraine, Cranial Nerve Disease, Oculomotor Nerve

Abstract

Background: Recurrent painful ophthalmoplegic neuropathy (RPON), formerly known as ophthalmoplegic migraine (OM), is a poorly understood condition that presents with recurrent unilateral headaches and at least one ocular cranial nerve (CN) palsy, generally in childhood. There has been ongoing debate about whether the etiology of this disorder is neuropathic or related to migraines.

The Case: We present a case about a 10-year-old male with his third presentation of RPON, repeatedly affecting his right oculomotor nerve. His treatment choices are discussed, along with associated outcomes. The patient was treated with topiramate with resolution of his symptoms occurred within one month.

Conclusion: As the annual incidence of RPON is rare at fewer than 1 case per million people, clear documentation of observed cases with treatment failures and successes is key to building evidence for future management.

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Author Biographies

Sharmila Segar, Medical College of Georgia, Augusta University, Augusta, Georgia, USA.

Sharmila Segar is a fourth year medical student at the Medical College of Georgia, pursuing a career in ophthalmology.

Chandni Duphare, Medical College of Georgia, Augusta University, Augusta, Georgia, USA.

Chandni Duphare is a fourth year medical student at the Medical College of Georgia, pursuing a career in ophthalmology.

Osemelu Aburime, Medical College of Georgia, Augusta University, Augusta, Georgia, USA.

Dr. Aburime is starting his glaucoma fellowship at Ochsner Health System.

References

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Published

2018-12-23

How to Cite

Segar, S., Duphare, C., & Aburime, O. (2018). Recurrent Painful Ophthalmoplegic Neuropathy Affecting Right Oculomotor Nerve in 10-Year-Old Male. Case Report. International Journal of Medical Students, 6(3), 114–117. https://doi.org/10.5195/ijms.2018.285

Issue

Vol. 6 No. 3 (2018)

Section

Case Report

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